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VALINE 50 Sachets Vitaflo 30x4gMSUD is an inherited metabolic disorder caused by branched chain ketoacid dehydrogenase (BCKD) deficiency, resulting in the accumulation of branched chain amino acids (BCAAs) L leucine, L isoleucine and L valine. MSUD varies considerably in disease severity, with clinical features including seizures, ketoacidosis, hypoglycaemia, apnoea, ataxia and coma. Elevated L leucine levels are toxic and associated with abnormal brain morphology and cognitive
MSUD is an inherited metabolic disorder caused by branched-chain α-ketoacid dehydrogenase (BCKD) deficiency, resulting in the accumulation of branched chain amino acids (BCAAs) L-leucine, L-isoleucine and L-valine. MSUD varies considerably in disease severity, with clinical features including seizures, ketoacidosis, hypoglycaemia, apnoea, ataxia and coma. Elevated L-leucine levels are toxic and associated with abnormal brain morphology and cognitive impairment. This may impact on social and psychomotor function.
The mainstay of dietary management is the restriction of dietary BCAAs, especially L-leucine, and the use of BCAA-free protein substitutes (PS). To promote anabolism of L-leucine, when L-leucine blood concentrations are high, additional supplementation with L-valine may be required. In addition, patients on dietary management can develop a L-valine deficiency, which is absent from their PS. This can lead to a rash and can also involve the eye and gut epithelium. Supplementation of the diet with L-valine is used to manage this.
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4.1 ★★★★★
Based on 20 reviews
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Product Reviews
★★★★★ 5
Fascinating and well written
Format: Hardcover
This is one of those books that makes you re-see everyday things with new awareness and a more critical eye. Well-researched, organized and written. Highly recommend!
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Reviewed in the United States on October 3, 2022
★★★★★ 1
Pop culture: yoga, croases, costumes, tattoos of sacred symbols …is not religious appropiation.
Format: Hardcover
Neither are Christmas trees, a pagan tradition, except to religious fundamentalists. Religion, all religions … which are all patriarchal by origin and definition is to be challenged for hypocrisy … see Madonna for in your face pop blasphemy. This is not scholarship.
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Reviewed in the United States on January 20, 2023
★★★★★ 5
An Invitation to Better Dialogue
Format: Paperback
Perry Schmidt-Leukel has tackled one of the most difficult intellectual minefields of all - religious pluralism. I admire his attempt, desire and intentions. This work is based off of a 2015 Gifford lecture in Glasgow.
Religious Pluralism is one of the three possible stances that address the Problem of Religious Diversity. The other two stances are significantly more common and also close sisters - Exclusivism and Inclusivism. Pluralism is the most radical stance but also one most needed in a globally-connected world with seemingly ineradicable conflict and violence.
One can safely ignore, by the way, the stance that all religions are nothing but projections of immature minds (Naturalism); this is a gaslighting position which tries to throw the baby out with the bathwater and does not really address the issue of religious diversity. Religion should be treated with the seriousness it is due and humans are inherently homo religiosus as history and culture attest.
There are several reasons why Pluralism should be considered the superior stance. First, it is the most pragmatic as alluded to in my above statement on conflict. Second, if one understands Truth as something that no human or group of humans can ever have a monopoly on then Pluralism makes more sense than the other two. I should add that we should approach understanding of Truth more as a peregrination than as some fixed or static destination.
Third, much of religious diversity is due to historical, cultural and especially linguistic differences but if we spend time in interreligious dialogue, we can begin to see that the religions are often saying the same things but using different jargon. The jargon should not be confused with Reality or Truth. As humans, we must continually be humbled by our lowly ability to understand reality as it is in itself and our immense limitations of language. Language too often creates division and can also circumscribe our ability to understand. Yet, it is all we really have to communicate with.
Perry spends some time first outlining what a program of sustained interreligious dialogue would look like and some foundational principles. He then addresses some of the biggest elephants in the room - The Son, The Prophet and The Buddha - and how we can approach possible reconciliation, or at least how we can begin to frame the discussion. The other main issue is the problem of a Creator God in Buddhism.
If I were to offer a point of criticism to Perry's approach it is that he does not include in his discussion Philosophical Religions such as Platonism/Neoplatonism and Panentheism. However, I understand that would have really complicated things and he clearly wanted to only focus on the main traditional religions.
Perry then finishes up with a very fresh and thought-provoking discussion on a fractal interpretation of religion. That may be the most profound chapter of the book.
The book is full of insight but should be taken as only an overview (albeit a very good one) and a hopeful beginning to more in-depth analysis and discussion. I look forward to reading more from Schmidt-Leukel and I hope more people can move from their exclusivist and inherently conflict-bound view of the world to a more peaceful and uniting view of the very same one reality we are all experiencing and are all a small part of.
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Reviewed in the United States on January 18, 2026
★★★★★ 5
Pluralism as a positive good
Format: Paperback
Anyone iterested in how religions might think of their co-religionists should read this book. It pushes at the boundaries of settled views and points the way to a different future for interreligious relations. One of the best books on the fiedl for some time.
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Reviewed in the United States on March 4, 2017
★★★★★ 5
Digital Detective Delight
Format: Paperback
Learn Computer Forensics is a standout resource that makes diving into digital investigations feel both exciting and achievable. Right from the first pages, you are drawn in with relatable scenarios...uncovering clues from a smartphone or piecing together a story from social media posts. The author’s warm, conversational style turns what could be a dry subject into a fascinating journey, making complex ideas like evidence preservation and chain of custody feel straightforward and even a little fun to explore.
As you work your way through the book, you’ll find clear, hands-on advice for setting up your own forensic workstation and choosing the right tools for the job. Chapters on Windows artifacts, RAM analysis, and email investigations guide you step by step. What makes these sections especially engaging is the way each lesson includes practical exercises. By winding your way through browser history or reconstructing email paths, you gain real skills instead of just theory. It feels less like following a checklist and more like cracking a case alongside a friendly mentor.
What really sets this edition apart is its human touch. The author peppers in personal anecdotes...like tips for sketching a crime scene or handling tricky insider-threat investigations...that add personality and context. You’ll walk away not only understanding how to pull data from a disk image but also why certain methods matter in real-life cases. If you want a forensics book that feels less like a textbook and more like a conversation with a seasoned investigator, this is it. It earns every one of its five stars.
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Reviewed in the United States on June 2, 2025
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